Dentinogenesis imperfecta type II: approach for dental treatment

Dentin is a major structural component of tooth and serves as the framework upon which enamel and cementum form. Dentin supports enamel via mechanical stress distribution through well‑organized dentinoenamel junctions. Heritable dentin defects are rare diseases that affect primarily the organic dentin matrix. They have been classified into three types of dentinogenesis imperfecta (DI-I, DI-II and DI-III), and two types of dentin dysplasia (DD-I and DD-II) both of which present autosomal dominant transmission that affects the primary and permanent dentition.

According to Shields et al. (1973), the DI type I is associate with osteogenesis imperfecta. DI type II is found in patients with dentition abnormalities alone and no bone disease. DI type III is the Brandywine form, named for the city Brandywine, Maryland, where there was a large population of patients with this disorder.