PDF: Capdepont's Teeth - a Hereditary Dentin Defect. Case Report & Review

Capedepont's teeth or hereditary opalescent teeth or dentinogenesis imperfecta (DGI) is a hereditary disorder in the absence of any other systemic disorder (Neville et al., 2009) affecting 1 in 8000 births.

(Bhandari & Pannu, 2008; Barron et al., 2008; Henke et al., 1999; Subramaniam et al., 2008; Yashoda Devi et al., 2011; Kamboj & Chandra, 2007). 

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It shows an autosomal dominant trait affecting both deciduous and permanent dentition (Subramaniam et al.; Shafer et al., 2009; Singh & Singh, 2004). 

Better understanding and treatment planning of this entity is possible if detected at the primary dentition level.

Dentinogenesis imperfecta is an autosomal dominant genetic disorder with abnormal dentin structure affecting both primary and permanent dentitions leading to discolouration and attrition of teeth.

Diagnosis is usually based on family history, a detailed clinical examination and pedigree construction. Treatment involves preservation of teeth, removal of infection, restoration of function and esthetics.

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