PDF: Prosthetic rehabilitation for a patient with hypohidrotic ectodermal dysplasia: a clinical case

Hypohidrotic ectodermal dysplasia (HED) is a hereditary syndrome, characterized by a classic triad of hypotrichosis, hypodontia and hypohidrosis.

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The case of an 8-year-old girl with HED presenting oligodontia and marked resorption of maxillary and mandibular alveolar ridges is reported. A specially designed aluminum wire tray was used for taking impressions of both dental arches. 

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Prosthetic rehabilitation included a removable maxillary overdenture and a mandibular conventional acrylic resin denture made tissue-compatible by means of a soft denture liner attached to denture base. The proposed treatment plan provided improved esthetics, function, and quality of life.

Ectodermal dysplasia (ED) is a group of hereditary diseases with abnormal development of two or more structures of ectodermal origin1.

These disorders are relatively rare with an incidence of 1 in 10,000 to 1 in 100,000 live births. ED can present numerous clinical alterations and up to 154 different types and 11 subgroups have been observed depending on the involvement of the hair, teeth, nails or sweat glands3. ED can be hypohidrotic or hidrotic depending on the sweat gland function.

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