PDF: Prosthetic rehabilitation for a patient with hypohidrotic ectodermal dysplasia: a clinical case

Hypohidrotic ectodermal dysplasia (HED) is a hereditary syndrome, characterized by a classic triad of hypotrichosis, hypodontia and hypohidrosis.

The case of an 8-year-old girl with HED presenting oligodontia and marked resorption of maxillary and mandibular alveolar ridges is reported.

A specially designed aluminum wire tray was used for taking impressions of both dental arches.

Prosthetic rehabilitation included a removable maxillary overdenture and a mandibular conventional acrylic resin denture made tissue-compatible by means of a soft denture liner attached to denture base. 

The proposed treatment plan provided improved esthetics, function, and quality of life.

Oral findings include total or partial anodontia affecting both the primary and the permanent dentitions. The teeth are usually conical or peg shaped. 

Alveolar ridges are underdeveloped resulting in reduced vertical dimension, thereby giving a senile facial appearance along with protuberant dry lips.

This paper describes the prosthetic rehabilitation of a child with HED presenting severely resorbed alveolar ridges by using specially designed aluminum trays and tissue-supported dentures.